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Prenatal Diagnosis of the Congenital High Airway Obstruction Syndrome: Case Report and Literature Review

Abstract

Clinical case of the congenital high airway obstruction syndrome in 19 weeks old fetus is presented. In literature review classification, pathophysiology, prenatal diagnosis, and treatment of the congenital high airway obstruction syndrome are shown. Main echography signs of the abnormality includes: bilateral enlargement of the lung size, increased lung echogenicity, dilated trachea with hypoechoic fluid, and protrusion of the diaphragm in to the abdomen. There is a high likelihood of the ascites due to compression of the great vessels and polyhydramnios due to esophagus compression. It is noted that prognosis for the newborn in the presence of this defect is unfavorable.

About the Authors

N. V. Mashinets
Research Center for Obstetrics, Gynecology and Perinatology
Russian Federation


V. N. Demidov
Research Center for Obstetrics, Gynecology and Perinatology
Russian Federation


E. P. Zatikyan
Research Center for Obstetrics, Gynecology and Perinatology
Russian Federation


References

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Review

For citations:


Mashinets N.V., Demidov V.N., Zatikyan E.P. Prenatal Diagnosis of the Congenital High Airway Obstruction Syndrome: Case Report and Literature Review. Ultrasound & Functional Diagnostics. 2015;(6):53-57. (In Russ.)

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ISSN 1607-0771 (Print)
ISSN 2408-9494 (Online)