Артериовенозные мальформации головного мозга у плода. Пренатальная ультразвуковая диагностика, лечение, прогноз

Проведен детальный литературный обзор, посвященный артериовенозной мальформации вены Галена с целью систематизации современных знаний по данной проблеме. Анализ данных включает анатомические, генетические, морфологические, патофизиологические аспекты, классификацию, клиническую картину, диагностику, постнатальный прогноз летальности и неврологических осложнений с учетом предикторов неблагоприятных исходов. Подробно описаны механизмы декомпенсации, обусловленные постнатальной перестройкой гемодинамики.

В статье также освещены современные методы лечения в неонатальном периоде.

Подчеркнута важность пренатального формирования групп риска и определения показаний к возможности внутриутробного хирургического лечения.

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